Pathways of ammonia detoxification to GLN in muscles associated with Increased usage on the BCAA and ?-KG (cataplerosis) and advised outcomes of BCAA and phenylbutyrate in subjects with liver cirrhosis or UCD. Positive result of BCAA on ammonia detoxification to GLN could be blunted by GLN degradation to ammonia in enterocytes and kidneys. Phenylbu